Bilateral Giant Adrenal Myelolipomas: a case report and literature review
نویسندگان
چکیده
Adrenal myelolipoma is a rare benign adrenal neoplasm presenting in 0.08%-0.4% of population based on autopsy series. It is of adrenal origin composed of mature adipose tissue and a variable amount of hematopoietic elements (myeloid and erythroid cells). Most patients are asymptomatic, and the lesion is discovered incidentally at autopsy or on imaging studies performed for other reasons. Most tumors are unilateral and small in size (< 5cm). The case of symptomatic bilateral giant adrenal myelolipomas is extremely rare. We report a case of bilateral giant adrenal myelolipoma in a 56-year-old male presenting w ith gradual ly abdom i na l d i s tent ion for 6 months. We present characteristic CT finding in this patient with review of literatures. Myelolipoma is a relatively rare benign tumor composed of fatty tissue and bone marrow elements. It is frequently arised from the adrenal glands but may exist as a solitary mass elsewhere. Adrenal myelolipomas are typically small in size (<5cm), nonfunctioning and asymptomatic. They are most often discovered incidentally [1]. We report a case of bilateral giant myelolipoma with presentation of gradually abdominal distention for 6 months.
منابع مشابه
Giant Bilateral Adrenal Myelolipoma with Congenital Adrenal Hyperplasia
Myelolipomas are rare and benign neoplasms, predominant of the adrenal glands, consisting of adipose and mature hematopoietic tissue, commonly discovered incidentally with increased use of radiologic imaging. Few cases of giant bilateral adrenal masses are reported, especially in the setting of congenital adrenal hyperplasia (CAH). We report the case of a 39-year-old male with a history of CAH ...
متن کاملGiant Adrenal Myelolipoma Presenting as an Incidentaloma: a Case Report and Review of Literature
Submit Manuscript | http://medcraveonline.com mixture of myeloid and erythroid cells. Generally myelolipomas occurs in adrenal gland, but it can be present in other sites also. In 1905, it was initially reported by Gierke and afterword’s Oberling coined the term “myelolipoma” in 1929 [1,2]. According to the available literature, Myelolipomas account for approximately 3 to 5% of all primary adre...
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Myelolipomas are rare benign tumors composed of mature fat and bone marrow elements, typically found in the adrenal gland, but have been reported in extra-adrenal locations. Adrenal myelolipoma seldom produces symptoms unless it attains considerable size or hemorrhage into itself. The origin of adrenal myelolipoma remains obscure, various theories have been proposed. Here, we present a case of ...
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BACKGROUND Although chronic adrenocorticotropic hormone (ACTH) and androgen hyperstimulation are assumed to be involved in the pathogenesis of adrenal myelolipomas associated with poor-compliance patients with congenital adrenal hyperplasia (CAH), the expression of their receptors has not yet been demonstrated in these tumors so far. METHODS We analyzed Melanocortin 2 receptor (MC2R), Androge...
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تاریخ انتشار 2008